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Autosomal Domit Mutilating Palmoplantar Keratoderma With Periorificial Keratotic Plaques

Disease ID: disease_node_19368

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DbxrefMIM:614594
SubclassofDOID_0050736, DOID_0112011
Data SourceDOID
SynonymsOLMS1, Olmsted syndrome 1, autosomal dominant Olmsted syndrome
Doid Labelautosomal domit mutilating palmoplantar keratoderma with periorificial keratotic plaques
Doid DescriptionA mutilating palmoplantar keratoderma with periorificial keratotic plaques that has_material_basis_in heterozygous mutation in the TRPV3 gene on chromosome 17p13.2.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_19368
Doid IdDOID_0112013
LabelAutosomal Domit Mutilating Palmoplantar Keratoderma With Periorificial Keratotic Plaques