Mutilating Palmoplantar Keratoderma With Periorificial Keratotic Plaques
Disease ID: disease_node_19367
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| Dbxref | GARD:4075, MEDDRA:10068842, ORDO:659 |
|---|---|
| Subclassof | DOID_161 |
| Data Source | DOID |
| Synonyms | OLMS, Olmsted syndrome, mutilating palmoplantar hyperkeratosis with periorificial keratotic plaques, palmoplantar and periorificial keratoderma |
| Doid Label | mutilating palmoplantar keratoderma with periorificial keratotic plaques |
| Doid Description | A keratosis characterized by a bilateral mutilating palmoplantar keratoderma and periorificial keratotic plaques with severe pruritus of lesions. |
| Disease Node Id | disease_node_19367 |
| Doid Id | DOID_0112011 |
| Label | Mutilating Palmoplantar Keratoderma With Periorificial Keratotic Plaques |
- Incoming r'ship
SUBCLASS_OFto/from X-Linked Mutilating Palmoplantar Keratoderma With Periorificial Keratotic Plaques(ID:disease_node_19369) (Disease) - Outgoing r'ship
SUBCLASS_OFto/from Keratosis(ID:disease_node_4454) (Disease) - Incoming r'ship
SUBCLASS_OFto/from Autosomal Domit Mutilating Palmoplantar Keratoderma With Periorificial Keratotic Plaques(ID:disease_node_19368) (Disease)