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Diamond-Blackfan Anemia 15 With Mandibulofacial Dysostosis

Disease ID: disease_node_15309

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DbxrefMIM:606164
SubclassofDOID_0050736, DOID_1339
Data SourceDOID
SynonymsDBA15
Doid LabelDiamond-Blackfan anemia 15 with mandibulofacial dysostosis
Doid DescriptionA Diamond-Blackfan anemia characterized by Diamond-Blackfan anemia and mandibulofacial dysostosis (micrognathia, downslanting palpebral fissures, submucosal cleft palate or bifid uvula, and malar hypoplasia) that has_material_basis_in heterozygous mutation in the RPS28 gene on chromosome 19p13.2.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_15309
Doid IdDOID_0111894
LabelDiamond-Blackfan Anemia 15 With Mandibulofacial Dysostosis