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Anemia, Diamond-Blackfan

Disease ID: disease_node_11027

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DbxrefGARD:6274, ICD10CM:D61.01, MESH:D029503, MIM:PS105650, NCI:C61236, ORDO:124
SubclassofDOID_1340
Data SourceDOID, MESH
SynonymsBlackfan - Diamond syndrome, chronic constitutional pure red cell anaemia
Mesh IdD029503
Mesh LabelAnemia, Diamond-Blackfan
Mesh SubclassofD029502, D012010
Doid LabelDiamond-Blackfan anemia
Doid DescriptionA pure red-cell aplasia that is characterized by anemia (low red blood cell counts) with decreased erythroid progenitors in the bone marrow and has_material_basis_insufficient levels of red blood cells due to bone marrow dysfunction. Xref MGI. OMIM mapping confirmed by DO. [SN].
Disease Node Iddisease_node_11027
Doid IdDOID_1339
LabelAnemia, Diamond-Blackfan