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Multiple Endocrine Neoplasia Type 2B

Disease ID: disease_node_9799

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DbxrefICD10CM:E31.23, ICD9CM:258.03, MESH:D018814, MIM:162300, NCI:C3227, ORDO:247709, SNOMEDCT_US_2023_03_01:61530001, UMLS_CUI:C0025269
SubclassofDOID_0050736, DOID_3125
Data SourceDOID, MESH
SynonymsMEN type IIB, MEN2B, Multiple endocrine neoplasia, type 3, Wagenmann-Froboese syndrome, mucosal neuroma syndrome
Mesh IdD018814
Mesh LabelMultiple Endocrine Neoplasia Type 2b
Mesh SubclassofD009377
Doid Labelmultiple endocrine neoplasia type 2B
Doid DescriptionA multiple endocrine neoplasia characterized by medullary thyroid carcinoma, pheochromocytoma, multiple mucosal neuromas and intestinal ganglioneuromas, and often a marfanoid habitus and other skeletal abnormalities. OMIM mapping confirmed by DO. [SN].
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_9799
Doid IdDOID_10016
LabelMultiple Endocrine Neoplasia Type 2B