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Pemphigus, Benign Familial

Disease ID: disease_node_8738

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DbxrefGARD:6559, ICD10CM:Q82.8, MESH:D016506, MIM:169600, NCI:C82865, SNOMEDCT_US_2023_03_01:79468000, UMLS_CUI:C0085106
SubclassofDOID_0050736, DOID_9182
Data SourceDOID, MESH
SynonymsBENIGN CHRONIC PEMPHIGUS, Pemphigus, Benign Familial
Disease Has LocationUBERON_8410021, UBERON_0015474
Mesh IdD016506
Mesh LabelPemphigus, Benign Familial
Mesh SubclassofD012872, D012873
Doid LabelHailey-Hailey disease
Doid DescriptionA pemphigus that is characterized by recurring blistering most commonly occurring in the folds of the skin, particularly the groin and axillary regions, and has_material_basis_in mutations in the ATP2C1 gene that result in loss of adhesion within the skin. Other sites of the body, such as the neck, perianal, and submammary regions, may likewise be affected. OMIM mapping confirmed by DO. [SN].
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_8738
Doid IdDOID_0050429
LabelPemphigus, Benign Familial