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Holoprosencephaly

Disease ID: disease_node_8636

Connections displayed (default: 10).
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DbxrefGARD:6665, ICD10CM:Q04.2, MESH:D016142, MIM:PS236100, NCI:C74988, ORDO:2162, SNOMEDCT_US_2023_03_01:30915001, UMLS_CUI:C0079541
SubclassofDOID_225, DOID_2490
Data SourceDOID, MESH
SynonymsHoloprosencephaly sequence
Mesh IdD016142
Mesh LabelHoloprosencephaly
Mesh SubclassofD000015, D061085, D025063, D019465
Doid Labelholoprosencephaly
Doid DescriptionA congenital nervous system abnormality characterized by failed or incomplete separation of the forebrain early in gestation, it is accompanied by a spectrum of characteristic craniofacial anomalies. Xref MGI. OMIM mapping confirmed by DO. [SN].
Disease Node Iddisease_node_8636
Doid IdDOID_4621
Disease Has Basis InSYMP_0000462
LabelHoloprosencephaly