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Tay-Sachs Disease

Disease ID: disease_node_7289

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DbxrefGARD:7737, ICD10CM:E75.02, MESH:D013661, MIM:272800, NCI:C85184, SNOMEDCT_US_2023_03_01:111385000, UMLS_CUI:C0039373
SubclassofDOID_3321
Data SourceDOID, MESH
SynonymsGM2 gangliosidosis, type 1, hexosaminidase A deficiency
Mesh IdD013661
Mesh LabelTay-Sachs Disease
Mesh SubclassofD020143
Doid LabelTay-Sachs disease
Doid DescriptionA GM2 gangliosidosis that is characterized onset in infancy of developmental retardation, followed by paralysis, dementia and blindness, with death in the second or third year of life and has_material_basis_in homozygous or compound heterozygous mutation in the alpha subunit of the hexosaminidase A gene (HEXA) on chromosome 15q23. OMIM mapping confirmed by DO. [SN].
Existence Starts DuringHP_0011463
Disease Node Iddisease_node_7289
Doid IdDOID_3320
LabelTay-Sachs Disease