This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Tangier Disease

Disease ID: disease_node_7280

Connections displayed (default: 10).
Loading graph...

DbxrefGARD:7731, ICD10CM:E78.6, MESH:D013631, MIM:205400, NCI:C85182, SNOMEDCT_US_2023_03_01:190783007, UMLS_CUI:C0039292
SubclassofDOID_1387
Data SourceDOID, MESH
Synonymsfamilial alpha-lipoprotein deficiency, familial high density lipoprotein deficiency
Mesh IdD013631
Mesh LabelTangier Disease
Mesh SubclassofD052456, D011115
Doid LabelTangier disease
Doid DescriptionA hypolipoproteinemia that is characterized by markedly reduced levels of plasma high density lipoproteins resulting in tissue accumulation of cholesterol esters and that has_material_basis_in homozygous or compound heterozygous mutation in the ABCA1 gene on chromosome 9q31. OMIM mapping confirmed by DO. [LS].
Disease Node Iddisease_node_7280
Doid IdDOID_1388
LabelTangier Disease