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Olivopontocerebellar Atrophies

Disease ID: disease_node_5684

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DbxrefMESH:D009849, NCI:C84947, SNOMEDCT_US_2023_03_01:67761004, UMLS_CUI:C0028968
SubclassofDOID_1289
Data SourceDOID, MESH
SynonymsDejerine-Thomas syndrome, Thomas' syndrome, WADIA-SWAMI SYNDROME
Mesh IdD009849
Mesh LabelOlivopontocerebellar Atrophies
Mesh SubclassofD019578, D013132
Doid Labelolivopontocerebellar atrophy
Doid DescriptionA neurodegenerative disease that is characterized by progressive cerebellar ataxia, leading to clumsiness in body movements, veering from midline when walking, wide-based stance, and falls without signs of paralysis or weakness and has_material_basis_in expansion of CAG triplet repeats (glutamine) resulting in degeneration of neuron in the cerebellum, pons and inferior olives. OMIM mapping confirmed by DO. [SN].
Disease Node Iddisease_node_5684
Doid IdDOID_14784
LabelOlivopontocerebellar Atrophies
Doid Alternate IdsDOID_12708