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Mucopolysaccharidosis Vi

Disease ID: disease_node_5274

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DbxrefGARD:7095, MESH:D009087, MIM:253200, NCI:C61264, SNOMEDCT_US_2023_03_01:69463008, UMLS_CUI:C0026709
SubclassofDOID_12798
Data SourceDOID, MESH
SynonymsMPS VI - Maroteaux-Lamy syndrome, Maroteaux - Lamy syndrome, Maroteaux-Lamy syndrome, arylsulfatase B deficiency, deficiency of N-acetylgalactosamine-4-sulfatase
Mesh IdD009087
Mesh LabelMucopolysaccharidosis VI
Mesh SubclassofD009083
Doid Labelmucopolysaccharidosis VI
Doid DescriptionA mucopolysaccharidosis characterized by a deficiency of the lysosomal enzyme N-acetylgalactosamine 4-sulfatase. OMIM mapping confirmed by DO. [SN].
Disease Node Iddisease_node_5274
Doid IdDOID_12800
LabelMucopolysaccharidosis Vi