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Alpha-Mannosidosis

Disease ID: disease_node_4992

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DbxrefGARD:6968, MESH:D008363, MIM:248500, NCI:C84548, SNOMEDCT_US_2023_03_01:65524005, UMLS_CUI:C0024748
SubclassofDOID_3211
Data SourceDOID, MESH
SynonymsAlpha-D-mannosidosis, alpha-mannosidase deficiency, deficiency of alpha-mannosidase
Mesh IdD008363
Mesh Labelalpha-Mannosidosis
Mesh SubclassofD044904
Doid Labelalpha-mannosidosis
Doid DescriptionA lysosomal storage disease that has_material_basis_in deficiency of the alpha-D-manosidase enzyme resulting in the impairment of cell function from a build up of complex sugars derived from glycoproteins in the lysosome. OMIM mapping confirmed by DO. [SN].
Disease Node Iddisease_node_4992
Doid IdDOID_3413
LabelAlpha-Mannosidosis