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Hyperlipoproteinemia Type I

Disease ID: disease_node_4796

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DbxrefMESH:D008072, MIM:207750, ORDO:309020, SNOMEDCT_US_2023_03_01:33513003, UMLS_CUI:C0268199, UMLS_CUI:C1720779
SubclassofDOID_0050737, DOID_0111417
Data SourceDOID, MESH
SynonymsC-II anapolipoproteinemia, familial APOC2 deficiency, familial apoC-II deficiency, hyperlipoproteinemia, type 1b, hyperlipoproteinemia, type Ib
Mesh IdD008072
Mesh LabelHyperlipoproteinemia Type I
Mesh SubclassofD008052, D006951
Doid Labelfamilial apolipoprotein C-II deficiency
Doid DescriptionA familial chylomicronemia syndrome characterized by onset in adolescence or adulthood of hypertriglyceridemia and fasting chylomicronemia that has_material_basis_in homozygous or compound heterozygous mutation in the APOC2 gene on chromosome 19q13.32.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_4796
Doid IdDOID_0111418
LabelHyperlipoproteinemia Type I