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Hemophilia A

Disease ID: disease_node_3828

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DbxrefGARD:6591, ICD10CM:D66, ICD9CM:286.0, MESH:D006467, MIM:306700, NCI:C27146, ORDO:98878, SNOMEDCT_US_2023_03_01:28293008, UMLS_CUI:C0019069
SubclassofDOID_0080012, DOID_0061030
Data SourceDOID, MESH
SynonymsCongenital factor VIII disorder, Hemophilia A, Subhemophilia, classic hemophilia, classic hemophilia A
Mesh IdD006467
Mesh LabelHemophilia A
Mesh SubclassofD020147, D025861, D006474
Doid Labelfactor VIII deficiency
Doid DescriptionA hemophilia that has_material_basis_in Factor VIII deficiency, which results in the formation of fibrin deficient clots which makes coagulation much more prolonged. OMIM mapping confirmed by DO. [SN].
Has Material Basis InGENO_0000149
Disease Node Iddisease_node_3828
Doid IdDOID_12134
LabelHemophilia A