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Glycogen Storage Disease Type Ii

Disease ID: disease_node_3516

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DbxrefGARD:5714, ICD10CM:E74.02, MESH:D006009, MIM:232300, NCI:C84734, SNOMEDCT_US_2023_03_01:237967002, UMLS_CUI:C0017921
SubclassofDOID_2747, DOID_0050737
Data SourceDOID, MESH
SynonymsGeneralized glycogenosis, Glycogen storage disease 2, Glycogen storage disease, type II, Glycogenosis, type 2, Lysosomal alpha-1,4-glucosidase deficiency, Pompe's disease, acid maltase deficiency, deficiency of glucoamylase, deficiency of maltase, glycogen storage disease type II
Mesh IdD006009
Mesh LabelGlycogen Storage Disease Type II
Mesh SubclassofD020140, D006008
Doid Labelglycogen storage disease II
Doid DescriptionA glycogen storage disease that has_material_basis_in deficiency of the lysosomal acid alpha-glucosidase enzyme resulting in damage to muscle and nerve cells due to an accumulation of glycogen in the lysosome. OMIM mapping confirmed by DO. [SN].
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_3516
Doid IdDOID_2752
LabelGlycogen Storage Disease Type Ii