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Fibrous Dysplasia, Polyostotic

Disease ID: disease_node_3262

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DbxrefGARD:6995, ICD10CM:Q78.1, ICD9CM:756.54, MESH:D005359, MIM:174800, NCI:C34610, SNOMEDCT_US_2023_03_01:205508003, UMLS_CUI:C0016065
SubclassofDOID_225, DOID_0050739
Data SourceDOID, MESH
Synonymsfibrous dysplasia of bone, osteitis fibrosa disseminata, polyostotic fibrous dysplasia
Mesh IdD005359
Mesh LabelFibrous Dysplasia, Polyostotic
Mesh SubclassofD005357
Doid LabelMcCune Albright syndrome
Doid DescriptionA syndrome that is characterized by polyostotic fibrous dysplasia, precocious puberty, and café-au-lait spots and has_material_basis_in spontaneous post zygotic missense mutation at ARG201 or Gln227 of the GNAS gene during embryogenesis. OMIM mapping confirmed by DO. [SN].
Has Material Basis InGENO_0000934
Disease Node Iddisease_node_3262
Doid IdDOID_1858
LabelFibrous Dysplasia, Polyostotic
Doid Alternate IdsDOID_11345