This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration. This website is for informational and educational purposes only. Please do not self-medicate; contact a medical professional for advice before administration.

Factor Xiii Deficiency

Disease ID: disease_node_3156

Connections displayed (default: 10).
Loading graph...

DbxrefGARD:10766, MESH:D005177, MIM:613225, MIM:613235, NCI:C98941, SNOMEDCT_US_2023_03_01:50189006, UMLS_CUI:C0015530
SubclassofDOID_0050737, DOID_1247
Data SourceDOID, MESH
SynonymsFactor XIII deficiency disease, Hereditary factor XIII deficiency disease, deficiency, Laki-Lorand factor
Mesh IdD005177
Mesh LabelFactor XIII Deficiency
Disease Has FeatureDOID_801
Mesh SubclassofD020147, D025861, D006474
Doid Labelfactor XIII deficiency
Doid DescriptionA blood coagulation disease that is characterized by easy bleeding, has_symptom prolonged umbilical cord bleeding, epistaxis, bleeding of the gums, menorrhagia, recurrent miscarriages, abnormal scar formation and wound healing, and hemarthrosis, and has_material_basis_in autosomal recessive inheritance of mutation of the F13A1 or F13B gene, which encodes Factor XIII, formally known as fibrin stabilizing factor. OMIM mapping confirmed by DO. [SN].
Has SymptomSYMP_0020021, SYMP_0000742, SYMP_0000007, SYMP_0020020, SYMP_0000448, SYMP_0000756
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_3156
Doid IdDOID_2211
LabelFactor Xiii Deficiency