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Factor Xi Deficiency

Disease ID: disease_node_3148

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DbxrefGARD:9670, ICD10CM:D68.1, ICD9CM:286.2, MESH:D005173, MIM:612416, NCI:C84705, SNOMEDCT_US_2023_03_01:49762007, UMLS_CUI:C0015523
SubclassofDOID_0061030, DOID_0050739
Data SourceDOID, MESH
SynonymsCongenital factor XI deficiency, Hereditary factor XI deficiency disease, Rosenthal's disease, hemophilia C, plasma thromboplastin antecedent deficiency
Mesh IdD005173
Mesh LabelFactor XI Deficiency
Mesh SubclassofD020147, D025861, D006474
Doid Labelfactor XI deficiency
Doid DescriptionA hemophilia that is characterized by deficiency of factor XI clotting factor and mild prolonged bleeding, especially of mucosal sites following trauma, and has_material_basis_in homozygous, compound heterozygous, or heterozygous mutation of the coagulation factor XI gene of chromosome 4q35.2. OMIM mapping confirmed by DO. [SN].
Has SymptomSYMP_0000007
Has Material Basis InGENO_0000934
Disease Node Iddisease_node_3148
Doid IdDOID_2229
LabelFactor Xi Deficiency