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Immunoglobulin Light-Chain Amyloidosis

Disease ID: disease_node_304

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DbxrefICD10CM:E85.81, MESH:D000075363
SubclassofDOID_409, DOID_557, DOID_655, DOID_9120, DOID_114
Data SourceDOID, MESH
SynonymsAL amyloidosis, Amyloidosis primary systemic, Light chain amyloidosis, Primary AL amyloidosis, Primary systemic AL amyloidosis, Primary systemic amyloidosis, Systemic AL amyloidsis
Disease Has LocationUBERON_0002113, UBERON_0000948, UBERON_0002107, UBERON_0001021
Mesh IdD000075363
Mesh LabelImmunoglobulin Light-chain Amyloidosis
Mesh SubclassofD054219, D000686, D010265, D008232
Doid Labelimmunoglobulin light chain amyloidosis
Doid DescriptionAn amyloidosis that is characterized by misfolded and aggregated amyloidogenic immunoglobulin light chains produced by marrow clonal plasma cells.
Disease Node Iddisease_node_304
Doid IdDOID_0080933
Disease Has Basis InSO_0001537
LabelImmunoglobulin Light-Chain Amyloidosis