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Dentinogenesis Imperfecta

Disease ID: disease_node_2440

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DbxrefGARD:6258, ICD10CM:K00.5, MESH:D003811, MIM:125490, MIM:125500, NCI:C84667, ORDO:49042, SNOMEDCT_US_2023_03_01:367461002, UMLS_CUI:C0011436
SubclassofDOID_0050736, DOID_1091
Data SourceDOID, MESH
Mesh IdD003811
Mesh LabelDentinogenesis Imperfecta
Mesh SubclassofD014071
Doid Labeldentinogenesis imperfecta
Doid DescriptionA tooth disease characterized by discolored, opalescent teeth that has_material_basis_in mutation in the DSPP gene on chromosome 4q22. OMIM mapping confirmed by DO. [SN].
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_2440
Doid IdDOID_4154
LabelDentinogenesis Imperfecta