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Cleidocranial Dysplasia

Disease ID: disease_node_2130

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DbxrefGARD:6118, ICD10CM:Q74.0, MESH:D002973, MIM:119600, MIM:216330, NCI:C75020, ORDO:1452, SNOMEDCT_US_2023_03_01:65976001, UMLS_CUI:C0008928
SubclassofDOID_2256, DOID_0050736
Data SourceDOID, MESH
SynonymsMarie-Sainton Disease, cleidocranial dysostosis
Mesh IdD002973
Mesh LabelCleidocranial Dysplasia
Mesh SubclassofD010009, D019465
Doid Labelcleidocranial dysplasia
Doid DescriptionAn osteochondrodysplasia that has_material_basis_in mutations in the RUNX2 gene which results_in undeveloped or absent located_in clavicle along with delayed closing of fontanels in the located_in skull. Xref MGI. OMIM mapping confirmed by DO. [SN].
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_2130
Doid IdDOID_13994
LabelCleidocranial Dysplasia