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Hemophilia B

Disease ID: disease_node_2097

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DbxrefGARD:8732, ICD10CM:D67, ICD9CM:286.1, MESH:D002836, MIM:306900, NCI:C26721, SNOMEDCT_US_2023_03_01:41788008, UMLS_CUI:C0008533
SubclassofDOID_0080012, DOID_0061030
Data SourceDOID, MESH
SynonymsCongenital factor IX deficiency, Congenital factor IX disorder, deficiency, functional factor IX, factor IX deficiency
Mesh IdD002836
Mesh LabelHemophilia B
Mesh SubclassofD020147, D040181, D025861, D006474
Doid Labelhemophilia B
Doid DescriptionA hemophilia that has_material_basis_in Factor IX deficiency, which makes coagulation much more prolonged. The disease is inherited as an X-linked recessive trait. OMIM mapping confirmed by DO. [SN].
Has Material Basis InGENO_0000149
Disease Node Iddisease_node_2097
Doid IdDOID_12259
LabelHemophilia B