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Ornithine Translocase Deficiency

Disease ID: disease_node_20550

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DbxrefGARD:2830, MIM:238970
SubclassofDOID_9252
Data SourceDOID
SynonymsHHH syndrome, Hyperornithinemia-Hyperammonemia-Homocitrullinuria (HHH) syndrome
Doid Labelornithine translocase deficiency
Doid DescriptionAn amino acid metabolic disorder that has_material_basis_in deficiency of ornithine translocase resulting in the accumulation of ammonia in the blood.
Has Material Basis InCHEBI_16134
Disease Node Iddisease_node_20550
Doid IdDOID_0050720
LabelOrnithine Translocase Deficiency