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Neu-Laxova Syndrome 2

Disease ID: disease_node_20547

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DbxrefMIM:616038
SubclassofDOID_0050721
Data SourceDOID
Doid LabelNeu-Laxova syndrome 2
Doid DescriptionA serine deficiency that is characterized by multiple fatal malformations including ichthyosis, microcephaly, central nervous system abnormalities, limb deformities, intrauterine growth restriction, proptosis, anasarca, and micrognathia, and has_material_basis_in autosomal recessive inheritance of mutation in the PSAT1 gene on chromosome 9q21.1, causing issues producing the amino acid serine.
Has SymptomSYMP_0000369
Disease Node Iddisease_node_20547
Doid IdDOID_0080075
LabelNeu-Laxova Syndrome 2