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Agat Deficiency

Disease ID: disease_node_20543

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DbxrefMIM:612718
SubclassofDOID_0050798, DOID_0050737
Data SourceDOID
SynonymsCerebral creatine deficiency syndrome 3, arginine glycine amidinotransferase deficiency
Doid LabelAGAT deficiency
Doid DescriptionAn amino acid metabolic disorder that has_material_basis_in a mutation in the GATM gene resulting in deficiency of arginine:glycine amidinotransferase which then limits creatine synthesis.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_20543
Doid IdDOID_0050712
LabelAgat Deficiency