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Hypervalinemia And Hyperleucine-Isoleucinemia

Disease ID: disease_node_20536

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DbxrefMIM:618850
SubclassofDOID_0050737, DOID_9252
Data SourceDOID
Synonymsbranched-chain aminotransferase 2 deficiency
Doid Labelhypervalinemia and hyperleucine-isoleucinemia
Doid DescriptionAn amino acid metabolic characterized by highly elevated plasma valine and leucine concentrations that has_material_basis_in compound heterozygous mutation in the BCAT2 gene on chromosome 19q13.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_20536
Doid IdDOID_0060950
LabelHypervalinemia And Hyperleucine-Isoleucinemia