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Congenital Glutamine Deficiency

Disease ID: disease_node_20535

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DbxrefGARD:9848, MIM:610015, ORDO:71278
SubclassofDOID_0050737, DOID_9252
Data SourceDOID
SynonymsGLND, congenital systemic glutamine synthase deficiency
Doid Labelcongenital glutamine deficiency
Doid DescriptionAn amino acid metabolic disorder characterized by onset at birth of encephalopathy, lack of normal development, seizures, and hypotonia associated with variable brain abnormalities that has_material_basis_in homozygous mutation in the GLUL gene on chromosome 1q25.3.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_20535
Doid IdDOID_0070544
LabelCongenital Glutamine Deficiency