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Mucolipidosis Iii Alpha/Beta

Disease ID: disease_node_20505

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DbxrefMIM:252600, ORDO:577
SubclassofDOID_0050737, DOID_0080488
Data SourceDOID
Synonymsmucolipidosis III, pseudo-Hurler polydystrophy
Doid Labelmucolipidosis III alpha/beta
Doid DescriptionA mucolipidosis that has_material_basis_in mutation in the gene encoding the alpha/beta-subunits precursor gene of GLcNAc-phosphotransferase.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_20505
Doid IdDOID_0080071
LabelMucolipidosis Iii Alpha/Beta