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Niemann-Pick Disease Type C1

Disease ID: disease_node_20498

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DbxrefGARD:7207, ICD10CM:E75.2, MIM:257220
SubclassofDOID_14504
Data SourceDOID
SynonymsNPC1
Doid LabelNiemann-Pick disease type C1
Doid DescriptionA Niemann-Pick disease that has_material_basis_in an autosomal recessive mutation of the NPC1 gene on chromosome 18q11.2.
Disease Node Iddisease_node_20498
Doid IdDOID_0070113
Disease Has Basis InSO_0001537
LabelNiemann-Pick Disease Type C1