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Immunodeficiency 51

Disease ID: disease_node_20453

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DbxrefMIM:613953
SubclassofDOID_0050737, DOID_612
Data SourceDOID
SynonymsCANDF5, IMD51, familial candidiasis 5
Doid Labelimmunodeficiency 51
Doid DescriptionA primary immunodeficiency disease characterized by onset of chronic mucocutaneous candidiasis in the first years of life and lack of cellular responses to stimulation with certain IL17 isoforms that has_material_basis_in homozygous or compound heterozygous mutation in the IL17RA gene on chromosome 22q11.1.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_20453
Doid IdDOID_0111996
LabelImmunodeficiency 51