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Immunodeficiency 65

Disease ID: disease_node_20443

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DbxrefMIM:618648
SubclassofDOID_0050737, DOID_612
Data SourceDOID
SynonymsIMD65, immunodeficiency 65, susceptibility to viral infections
Doid Labelimmunodeficiency 65
Doid DescriptionA primary immunodeficiency disease characterized by onset in early infancy of recurrent and severe viral infections, impaired cellular type I interferon response, and poor outcomes after vaccination with live attenuated vaccines that has_material_basis_in homozygous or compound heterozygous mutation in the IRF9 gene on chromosome 14q12.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_20443
Doid IdDOID_0111978
LabelImmunodeficiency 65