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C1 Inhibitor Deficiency

Disease ID: disease_node_20437

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SubclassofDOID_626
Data SourceDOID
SynonymsQuincke edema
Doid LabelC1 inhibitor deficiency
Doid DescriptionA complement deficiency that is a functional deficiency in the complement component C1 inhibitor leading to hereditary angioedema (HAE) involving swelling due to leakage of fluid from blood vessels into connective tissue.
Disease Node Iddisease_node_20437
Doid IdDOID_0060002
LabelC1 Inhibitor Deficiency