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Congenital Disorder Of Glycosylation Iaa

Disease ID: disease_node_20420

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DbxrefMIM:617082
SubclassofDOID_0050737, DOID_0050570
Data SourceDOID
Synonymscongenital disorder of glycosylation 1aa
Doid Labelcongenital disorder of glycosylation Iaa
Doid DescriptionA congenital disorder of glycosylation I that is characterized by fibroblasts with reduced dolichol profiles and enhanced accumulation of free cholesterol and has_material_basis_in homozygous mutation in the NUS1 gene on chromosome 6q22.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_20420
Doid IdDOID_0080553
Disease Has Basis InHP_0001197
LabelCongenital Disorder Of Glycosylation Iaa