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Xeroderma Pigmentosum Group D

Disease ID: disease_node_20380

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DbxrefICD10CM:Q82.1, MIM:278730
SubclassofDOID_0050427
Data SourceDOID
SynonymsXP group D, XP group H, XP4, XP8, XPD, XPDC, XPH, xeroderma pigmentosum IV, xeroderma pigmentosum VIII
Doid Labelxeroderma pigmentosum group D
Doid DescriptionA xeroderma pigmentosum that has_material_basis_in homozygous or compound heterozygous mutation in the excision repair gene ERCC2 on chromosome 19q13.
Disease Node Iddisease_node_20380
Doid IdDOID_0110845
LabelXeroderma Pigmentosum Group D