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Short Stature, Hearing Loss, Retinitis Pigmentosa, And Distinctive Facies

Disease ID: disease_node_20347

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DbxrefMIM:617763, ORDO:494439
SubclassofDOID_225, DOID_0050737
Data SourceDOID
Doid Labelshort stature, hearing loss, retinitis pigmentosa, and distinctive facies
Doid DescriptionA syndrome that is characterized by short stature, brachydactyly, dysmorphic facial features, hearing loss, and visual impairment and that has_material_basis_in homozygous or compound heterozygous mutation in the EXOSC2 gene on chromosome 9q34.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_20347
Doid IdDOID_0081175
LabelShort Stature, Hearing Loss, Retinitis Pigmentosa, And Distinctive Facies