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Warsaw Breakage Syndrome

Disease ID: disease_node_20331

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DbxrefGARD:13708, MIM:613398, ORDO:280558
SubclassofDOID_225, DOID_0050737
Data SourceDOID
SynonymsWABS
Doid LabelWarsaw breakage syndrome
Doid DescriptionA syndrome mainly characterized by severe congenital microcephaly, growth restriction, and sensorineural hearing loss due to cochlear hypoplasia and that has_material_basis_in homozygous or compound heterozygous mutation in the DDX11 gene on chromosome 12p11.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_20331
Doid IdDOID_0060535
LabelWarsaw Breakage Syndrome