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Opitz Gbbb Syndrome

Disease ID: disease_node_20283

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DbxrefGARD:193, KEGG:H00583, MIM:300000
SubclassofDOID_0080012, DOID_225
Data SourceDOID
SynonymsOpitz G/BBB Syndrome, Opitz GBBB syndrome type I
Doid LabelOpitz GBBB syndrome
Doid DescriptionA syndrome that is a congenital midline malformation syndrome that is characterized by hypertelorism, hypospadias, cleft lip/palate, laryngotracheoesophageal abnormalities, imperforate anus, developmental delay, and cardiac defects and that has_material_basis_in mutation in the MID1 gene on chromosome Xp22.
Has Material Basis InGENO_0000149
Disease Node Iddisease_node_20283
Doid IdDOID_0080697
LabelOpitz Gbbb Syndrome
Doid Alternate IdsDOID_0050780