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Sandestig-Stefanova Syndrome

Disease ID: disease_node_20269

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DbxrefMIM:618804
SubclassofDOID_225, DOID_0050737
Data SourceDOID
Doid LabelSandestig-Stefanova syndrome
Doid DescriptionA syndrome that is characterized by microcephaly, trigonocephaly, congenital cataracts, microphthalmia, facial findings, camptodactyly, periventricular white matter loss, thin corpus callosum, delayed myelination, and poor prognosis and that has_material_basis_in homozygous mutation in the NUP188 gene on chromosome 9q34.
Has Material Basis InSO_0002054, GENO_0000148
Disease Node Iddisease_node_20269
Doid IdDOID_0081272
Disease Has Basis InSO_0000704
LabelSandestig-Stefanova Syndrome