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Immunodeficiency-Centromeric Instability-Facial Anomalies Syndrome 1

Disease ID: disease_node_20260

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DbxrefICD10CM:D84.8, MIM:242860
SubclassofDOID_0090007
Data SourceDOID
SynonymsICF syndrome 1
Doid Labelimmunodeficiency-centromeric instability-facial anomalies syndrome 1
Doid DescriptionAn immunodeficiency-centromeric instability-facial anomalies syndrome characterized by autosomal recessive inheritance, facial dysmorphism and immunoglobulin deficiency of lymphocytes that has_material_basis_in homozygous or compound heterozygous mutation in the DNMT3B gene on chromosome 20q11.2.
Disease Node Iddisease_node_20260
Doid IdDOID_0090008
LabelImmunodeficiency-Centromeric Instability-Facial Anomalies Syndrome 1