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Immunodeficiency-Centromeric Instability-Facial Anomalies Syndrome 4

Disease ID: disease_node_20257

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DbxrefICD10CM:D84.8, MIM:616911
SubclassofDOID_0090007
Data SourceDOID
SynonymsICF syndrome 4
Doid Labelimmunodeficiency-centromeric instability-facial anomalies syndrome 4
Doid DescriptionAn immunodeficiency-centromeric instability-facial anomalies syndrome characterized by autosomal recessive inheritance, recurrent infections in childhood and variable dysmorphic facial features that has_material_basis_in homozygous or compound heterozygous mutation in the HELLS gene on chromosome 10q23.
Disease Node Iddisease_node_20257
Doid IdDOID_0090011
LabelImmunodeficiency-Centromeric Instability-Facial Anomalies Syndrome 4