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Igsf1 Deficiency Syndrome

Disease ID: disease_node_20251

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DbxrefICD10CM:E03.1, MIM:300888, ORDO:329235
SubclassofDOID_0080012, DOID_225
Data SourceDOID
SynonymsCHTE, X-linked central congenital hypothyroidism with late-onset macroorchidism, X-linked central congenital hypothyroidism with late-onset testicular enlargement, central hypothyroidism and testicular enlargement
Doid LabelIGSF1 deficiency syndrome
Doid DescriptionA syndrome characterized by hypothyroidism that is present at birth, delayed testosterone increase in puberty, and testicular enlargement in adulthood that has_material_basis_in mutation of the IGSF1 gene on chromosome Xq26.
Has Material Basis InGENO_0000149
Disease Node Iddisease_node_20251
Doid IdDOID_0111140
LabelIgsf1 Deficiency Syndrome