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High Myopia-Sensorineural Deafness Syndrome

Disease ID: disease_node_20240

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DbxrefGARD:12844, MIM:221200, ORDO:363396
SubclassofDOID_225, DOID_0050737
Data SourceDOID
SynonymsDFNMYP, deafness and myopia, deafness and myopia syndrome
Doid Labelhigh myopia-sensorineural deafness syndrome
Doid DescriptionA syndrome characterized by severe myopia and moderate to profound, bilateral, progressive sensorineural hearing loss that has_material_basis_in homozygous or compound heterozygous mutation in the SLITRK6 gene on chromosome 13q31.1.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_20240
Doid IdDOID_0111628
LabelHigh Myopia-Sensorineural Deafness Syndrome