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Tetraamelia Syndrome 1

Disease ID: disease_node_20230

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DbxrefGARD:5148, MIM:273395
SubclassofDOID_0112191, DOID_0050737
Data SourceDOID
SynonymsTETAMS1, tetra-amelia syndrome 1
Doid Labeltetraamelia syndrome 1
Doid DescriptionA tetraamelia syndrome characterized by complete limb agenesis without defects of scapulae or clavicles that has_material_basis_in homozygous or compound heterozygous mutation in WNT3 on chromosome 17q21.31-q21.32.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_20230
Doid IdDOID_0112192
LabelTetraamelia Syndrome 1