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Ghosal Hematodiaphyseal Syndrome

Disease ID: disease_node_20224

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DbxrefGARD:10297, MIM:231095, ORDO:1802
SubclassofDOID_225, DOID_0050737
Data SourceDOID
SynonymsGhosal hematodiaphyseal dysplasia, Ghosal syndrome, diaphyseal dysplasia-anemia syndrome
Doid LabelGhosal hematodiaphyseal syndrome
Doid DescriptionA syndrome characterized by increased bone density with predomit diaphyseal involvement and aregenerative corticosteroid-sensitive anemia that has_material_basis_in homozygous or compound heterozygous mutation in TBXAS1 on chromosome 7q34.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_20224
Doid IdDOID_0112251
LabelGhosal Hematodiaphyseal Syndrome