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Beare-Stevenson Cutis Gyrata Syndrome

Disease ID: disease_node_20166

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DbxrefGARD:332, MIM:123790
SubclassofDOID_0050736, DOID_225
Data SourceDOID
Doid LabelBeare-Stevenson cutis gyrata syndrome
Doid DescriptionA syndrome that is characterized by cutis gyrata, acanthosis nigricans and craniosynostosis, has_material_basis_in heterozygous mutation in the FGFR2 gene on chromosome 10q26. OMIM mapping confirmed by DO. [SN].
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_20166
Doid IdDOID_0050660
LabelBeare-Stevenson Cutis Gyrata Syndrome