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Wolfram Syndrome 1

Disease ID: disease_node_20160

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DbxrefICD10CM:E13.8, MIM:222300
SubclassofDOID_0050737, DOID_10632
Data SourceDOID
SynonymsDIDMOAD, WFS1, diabetes mellitus AND insipidus with optic atrophy AND deafness
Doid LabelWolfram syndrome 1
Doid DescriptionAn autosomal recessive disease that is characterized by diabetes mellitus, optic atrophy, and deafness as well as various other possible disorders and has_material_basis_in autosomal recessive inheritance of homozygous or compound heterozygous mutation in the WFS1 gene on chromosome 4p16.1.
Has Material Basis InGENO_0000148
Disease Node Iddisease_node_20160
Doid IdDOID_0110629
LabelWolfram Syndrome 1