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Congenital Generalized Lipodystrophy Type 4

Disease ID: disease_node_20149

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DbxrefGARD:10937, ICD10CM:E88.1, MIM:613327, ORDO:228429
SubclassofDOID_0050585
Data SourceDOID
SynonymsBerardinelli-Seip congenital lipodystrophy type 4 with muscular dystrophy, congenital generalised lipodystrophy type 4, generalised congenital lipodystrophy type 4, generalised congenital lipodystrophy with myopathy, generalized congenital lipodystrophy type 4, generalized congenital lipodystrophy with myopathy
Doid Labelcongenital generalized lipodystrophy type 4
Doid DescriptionA congenital generalized lipodystrophy that has_material_basis_in an autosomal recessive mutation of CAVIN1 on chromosome 17q21.2.
Disease Node Iddisease_node_20149
Doid IdDOID_0111138
Disease Has Basis InHP_0001197
LabelCongenital Generalized Lipodystrophy Type 4