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Immunodeficiency 11B

Disease ID: disease_node_20007

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DbxrefMIM:617638, NCI:C176630, UMLS_CUI:C4539957
SubclassofDOID_0050736, DOID_11200
Data SourceDOID
SynonymsIMD11B, atopic dermatitis, elevated IgE, and eosinophilia, immunodeficiency 11B with atopic dermatitis
Doid Labelimmunodeficiency 11B
Doid DescriptionA T cell deficiency characterized by defects in T-cell activation, increased IgE, eosinophilia and early childhood onset of moderate to severe atopic dermatitis that has_material_basis_in heterozygous mutation in the CARD11 gene on chromosome 7p22.2.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_20007
Doid IdDOID_0111958
LabelImmunodeficiency 11B