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X-Linked Immunodeficiency 74

Disease ID: disease_node_20005

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DbxrefMIM:301051
SubclassofDOID_0080012, DOID_11200
Data SourceDOID
SynonymsIMD74, TLR7 deficiency, X-linked immunodeficiency 74,COVID-19-related, respiratory insufficiency due to SARS-CoV-2 viral infection
Doid LabelX-Linked immunodeficiency 74
Doid DescriptionA T cell deficiency characterized by severe respiratory insufficiency in response to infection with the COVID19 coronavirus and impaired signaling through the TLR7 pathway that has_material_basis_in hemizygous mutation in the TLR7 gene on chromosome Xp22.2.
Has Material Basis InGENO_0000149
Disease Node Iddisease_node_20005
Doid IdDOID_0112063
LabelX-Linked Immunodeficiency 74