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Congenital Symmetric Circumferential Skin Creases 1

Disease ID: disease_node_19999

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DbxrefMIM:156610
SubclassofDOID_0050736, DOID_0112241
Data SourceDOID
SynonymsCSCSC1
Doid Labelcongenital symmetric circumferential skin creases 1
Doid DescriptionA multiple benign circumferential skin creases on limbs characterized by folding of excess skin, which leads to ringed creases, primarily of the limbs, intellectual disability, cleft palate, and dysmorphic features that has_material_basis_in heterozygous mutation in the TUBB gene on chromosome 6p21.33.
Has Material Basis InGENO_0000147
Disease Node Iddisease_node_19999
Doid IdDOID_0112242
LabelCongenital Symmetric Circumferential Skin Creases 1